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Neuropathies panel genome

Broj gena

280

TAT (radni dani)

25

Metoda

NGS uključujući analizu CNV-a

Uzorak

Puna krv

Opis

Neuropatije panel Genome uključuje gene povezane sa svim tipovima Charcot-Marie-Tooth bolesti i naslijeđenim neuropatijama malih vlakana. Ovaj panel uključuje skrining ekspanzije ponavljanja gena AR, ATXN1, ATXN10, ATXN2, ATXN3, ATXN7, DMPK, FMR1, FXN, NOP56, PPP2R2B, PRNP, kao i CNV analizu gena SMN1.

Geni

AARS1, ABCA1, ABCC9, ABHD12, ACTC1, ACTN2, AGTPBP1, AGXT, AIFM1, ALDH3A2, ALS2, AP1S1, APOA1, APTX, AR, ARL6IP1, ARSA, ASAH1, ATL1, ATL3, ATM, ATP1A1, ATP7A, ATXN1, ATXN10, ATXN2, ATXN3, ATXN7, B4GALNT1, BAG3, BCKDHB, BICD2, BRAF, BSCL2, C19orf12, CASQ2, CAV3, CD59, CHCHD10, CNTNAP1, COA7, COQ8A, COX6A1, CPOX, CRYAB, CSRP3, CTDP1, CYP27A1, DARS2, DCTN1, DEGS1, DES, DGUOK, DHH, DHTKD1, DMD, DMPK, DNAJB2, DNAJC3, DNM2, DNMT1, DRP2, DSC2, DSG2, DSP, DST, DSTYK, DYNC1H1, EGR2, ELP1, EMD, ERBB3, ERCC6, ERCC8, ETFDH, EXOSC3, EXOSC8, FA2H, FAH, FBLN5, FBXO38, FGD4, FGF14, FIG4, FKTN, FLVCR1, FMR1, FXN, GAA, GALC, GAN, GARS1, GBA2, GDAP1, GJB1, GJC2, GLA, GLE1, GNB4, HADHA, HADHB, HARS1, HINT1, HK1, HMBS, HRAS, HSPB1, HSPB8, HYCC1, IARS2, IGHMBP2, INF2, ITPR1, JAG1, JPH2, JUP, KARS1, KCNA1, KCNA2, KCNC3, KIF1A, KIF1B, KIF5A, KRAS, L1CAM, LAMA4, LAMP2, LAS1L, LDB3, LITAF, LMNA, LRP12, LRSAM1, LYST, MAP1B, MAP2K1, MAP2K2, MARS1, MCM3AP, MED25, MFN2, MMACHC, MME, MORC2, MPV17, MPZ, MRE11, MT-ATP6, MT-RNR1, MT-TL1, MTMR2, MTRFR, MTTP, MYBPC3, MYH14, MYH6, MYH7, MYL2, MYL3, MYPN, NAGA, NAGLU, NDRG1, NEFH, NEFL, NEXN, NGF, NIPA1, NOP56, NRAS, NTRK1, OPA1, OPA3, PDHA1, PDK3, PDYN, PEX10, PEX7, PHYH, PKP2, PLEKHG5, PLN, PLP1, PMM2, PMP2, PMP22, PNKP, PNPLA6, POLG, POLR3A, PPOX, PPP2R2B, PRDM12, PRKAG2, PRKCG, PRNP, PRPS1, PRX, PTEN, PTPN11, PTRH2, RAB7A, RAF1, RBM20, REEP1, RETREG1, RIT1, RYR2, SACS, SBF1, SBF2, SCARB2, SCN11A, SCN5A, SCN9A, SCP2, SCYL1, SELENOI, SEPTIN9, SETX, SGCD, SH3TC2, SIGMAR1, SIL1, SLC12A6, SLC1A3, SLC25A19, SLC25A46, SLC52A2, SLC52A3, SLC5A7, SMN1, SNRPN, SORD, SOS1, SOX10, SPART, SPAST, SPG11, SPG21, SPG7, SPTBN2, SPTBN4, SPTLC1, SPTLC2, SUCLA2, SURF1, SYT2, TAFAZZIN, TCAP, TDP1, TFG, TMEM43, TNNC1, TNNI3, TNNT2, TPM1, TRIP4, TRPV4, TTBK2, TTN, TTPA, TTR, TUBB3, TWNK, TYMP, UBA1, VAPB, VCL, VCP, VPS13A, VRK1, VWA1, WARS1, WASHC5, WNK1, XK, XPA, YARS1, ZFYVE26

 

NEUROLOŠKI PANELI