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Dementia panel exome

Broj gena

243

TAT (radni dani)

25

Metoda

NGS uključujući analizu CNV-a

Uzorak

Puna krv

Opis

Panel za demenciju uključuje gene povezane sa familijarnim oblicima Alzheimerove bolesti, degeneracijom frontalnog i temporalnog režnja i vaskularnom demencijom, neuro-mišićnim bolestima i poremećajima pokreta povezanim sa kognitivnim deficitima (npr. ALS-dementni kompleks, naslijeđeni oblici Parkinsonove bolesti i hiperkinetički poremećaji). Napominjemo da se u ovom panelu varijante u genima ATXN1, ATXN2, C9orf72 i PRNP ispituju samo kao sekvencijske varijante. Ako postoji klinička sumnja na poremećaj ekspanzije ponavljanja povezan sa ATXN1, ATXN2, C9orf72 ili PRNP, preporučuje se Genome verzija ovog panela.

Geni

ABCA1, ABCC6, ABCD4, ACE, ACOX2, ADAM10, AKAP9, ALG1, ALPL, ALS2, AMH, ANG, ANGPTL3, ANK3, ANXA11, APOB, APOE, APP, ARHGAP31, ARPC1B, ARSA, ASCC1, ASRGL1, ASXL3, ATL1, ATP7B, ATXN1, ATXN2, BCKDK, BICD2, BIN1, BLOC1S3, BRCA2, BRD4, BSCL2, C5, C9orf72, CASP10, CCNF, CD2AP, CELF2, CELSR1, CEP290, CHCHD10, CHMP2B, CHRNA3, CHRNA4, CIC, CLCN1, CLIC5, COG4, COQ4, CP, CPA1, CRBN, CSF1R, CTSC, CUBN, CYLD, CYP27A1, DAAM2, DAO, DCTN1, DEF6, DNM1, DSG2, DTYMK, DYSF, ENO3, ERBB4, ERLIN2, EWSR1, EXOSC5, FBP1, FIG4, FN1, FOXG1, FOXRED1, FTL, FUS, GABBR2, GANAB, GCDH, GLE1, GLIS3, GPAA1, GRN, HELLS, HEXA, HFE, HID1, HMOX1, HNRNPA1, HNRNPA2B1, HSPD1, IFT140, ITGA8, ITM2B, JAG2, JPH2, KANSL1, KIF5A, KMT2E, KMT5B, KRT86, LAMC3, LRRK2, LTBP4, MAGI2, MAPK8IP3, MAPT, MATR3, MCM8, MEF2C, MMP20, MMP21, MSH3, MT-ATP6, MT-ATP8, MT-CO1, MT-CO2, MT-CO3, MT-CYB, MT-ND1, MT-ND2, MT-ND3, MT-ND4, MT-ND4L, MT-ND5, MT-ND6, MT-RNR1, MT-RNR2, MT-TA, MT-TC, MT-TD, MT-TE, MT-TF, MT-TG, MT-TH, MT-TI, MT-TK, MT-TL1, MT-TL2, MT-TM, MT-TN, MT-TP, MT-TQ, MT-TR, MT-TS1, MT-TS2, MT-TT, MT-TV, MT-TW, MT-TY, MTHFD1, MTO1, MYH9, MYRF, MYT1L, NANS, NEFH, NEK1, NOTCH3, NPC1, OBSCN, OGDH, OPTN, PACS2, PANK2, PAX2, PCSK9, PEX5, PFN1, PGAP3, PHGDH, PHIP, PIGU, PIP5K1C, PLAU, PLCG2, POLR3B, PRKAR1B, PRNP, PSEN1, PSEN2, PSMC3, PSTPIP1, QRICH2, QRSL1, RARS1, RBFOX2, REEP1, REL, RUSC2, SCAPER, SCN4A, SDCCAG8, SERAC1, SETD1B, SETX, SIGMAR1, SLC24A1, SLC24A4, SLC52A3, SMAD3, SNCA, SNCB, SOD1, SORL1, SPAST, SPATA7, SPEN, SPG11, SPTB, SQSTM1, SS18L1, STAB1, STARD7, STT3A, TARDBP, TBK1, TCOF1, TET3, TFG, TIA1, TMEM106B, TP53, TREM2, TRMT1, TSPOAP1, TTN, TUBA4A, TULP1, TYROBP, UBE3A, UBQLN2, VAPB, VCP, VKORC1, VPS13C, WASHC5, WDR11, WDR73

 

NEUROLOŠKI PANELI